Aortic valve disease in adults has many etiologies and requires careful operative planning when severe enough to require intervention. A common cause of aortic valve dysfunction in adults is a congenitally bicuspid valve that may also be associated with aortic aneurysm. Here, we describe the presentation and management of a middle-aged woman with symptomatic severe aortic stenosis due to a bicuspid aortic valve. She required an aortic valve replacement as well as replacement of an aneurysmal ascending aorta and closure of a patent foramen ovale (PFO).